Case Report A case of retiform-hemangioendothelioma with unusual presentation and aggressive clinical features
Guiying Zhang, Qianjin Lu, Heng Yin, Haiquan Wen, Yuwen Su, Daiqiang Li, Rong Xiao
Departments of Anatomical Pathology, Surgery and 3Medical Oncology, Royal Melbourne Hospital, Victoria, Australia
Received April 12, 2010, accepted May 3, 2010, available online May 12, 2010
Abstract: Retiform hemangioendothelioma(RH) is an extremely rare low-grade angiosarcoma mainly involving the skin and subcutaneous tissue. Clinically patients often present with an asymptomatic slow-growing solitary nodular or plaque-like lesion. RH is characterized by frequent local recurrences but a very low metastatic rate. Here we reported a case of RH in a 61-year-old Chinese woman who presented with a rapid growing cutaneous plaque-like lesion on her right scalp, followed by another lesion behind the right ear. The lesions were associated with paroxysmal sharp needle-stabbing like headache. She underwent wide excision and skin engraftment. Three months post surgery, she experienced tumor recurrence, and died 9 months after the initial diagnosis. (IJCEP1004002).
Address all correspondence to: Rong Xiao, MD, PhD Department of Dermatology Second Xiangya Hospital of Central South University 139 Renming Rd, Changsha, Hunan 410011, PR China. Tel: (86 )-731 8529 5660. E-mail: email@example.com